Dynamic T-wave Changes with Hump Appearance from a Higher Intercostal Space in a Short QT Syndrome

Short QT syndrome (SQTS) is an inherited channelopathy associated with marked shortened QT intervals and sudden cardiac death. It is imperative for physicians to recognise the clinical features of the SQTS in making a timely correct diagnosis; however, the diagnosis of SQTS is further complicated by the presence of an overlapping range of QT intervals between affected cases and apparently healthy subjects. We present a case of SQTS with dynamic T-wave changes and T-wave hump appearance in the higher intercostal recordings, and speculate that these dynamic changes are a surrogate marker of underlying repolarisation abnormality and may help in the diagnosis of SQTS.